Orbital inflammatory disease: report of fourteen cases
DOI:
https://doi.org/10.36829/63CTS.v12i2.1918Keywords:
Dystrophin, Gowers, Myopathy, Pseudohypertroph, CPKAbstract
Inflammatory orbital disease (IOD) is considered a benign, non-infectious syndrome, which is characterized
by the presence of inflammatory symptoms and signs adjacent to or in the ocular orbit. It is rare and has
been reported to occur between 5-8% of cases all orbital masses. It can present as a manifestation in a specific
disease or as proposed by the classic description of “orbital pseudotumor” (idiopathic orbital inflammatory disease-
IOID), without a specific cause. The search for etiology is the main objective of analysis for this series of
cases; it constitutes a clinical challenge, as it is a diagnosis of exclusion with few clues that allow its identification.
We present fourteen cases that were seen during the period 2023-2025 at the rheumatology clinic of Roosevelt
Hospital. The following diagnoses were established: in 36% no cause was found (EIOI), IgG4-related disease
(ERIgG4) in 36%, Sjögren’s Syndrome in 21% and Systemic Lupus Erythematosus in 7%. In conclusion, in this
series the increase in cases associated with IgG4 syndrome and the favorable response in 100% of cases to the
use of corticosteroids (CO) are relevant.
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